Recommendations for the nutrition management of phenylalanine hydroxylase deficiency

Serum: Aqua (Water), Propylene Glycol, PEG-8, Glycerin, Glutathione, Ascorbyl Tetraisopalmitate, Sucrose, Cellulose Gum, Chondrus Crispus (Carrageenan) Extract, Ceratonia Siliqua Gum, Kojic Acid, Butylene Glycol, PPG-26-Buteth-26, PPG-8-Ceteth-20, PPG-4-Ceteth-20, PEG-40 Hydrogenated Castor Oil, Polysorbate 20, Deceth-7, Benzophenone-4, Disodium EDTA, Tocopherol, Citric Acid, Sodium Citrate, Sodium Dehydroacetate, Sodium Sulfite, Sodium Metabisulfite, Phenoxyethanol, Methylparaben, Chlorphenesin, Parfum (Fragrance), CI 19140 (Yellow 5), Benzyl Alcohol Milk: Aqua (Water), Paraffinum Liquidum (Mineral Oil), Glyceryl Stearate SE, Glycerin, Stearic Acid, Palmitic Acid, Parfum (Fragrance), Glutathione, Ascorbyl Tetraisopalmitate, Diacetyl Boldine, Cetearyl Alcohol, Caprylic/Capric Triglyceride, Disodium EDTA, Carbomer, Triethanolamine, Phenoxyethanol, Methylparaben, Ethylparaben, Propylparaben, Imidazolidinyl Urea, Alpha-Isomethyl Ionone, Benzyl Alcohol The lists of ingredients used in the composition of the FAIR & WHITE brand products are regularly updated

10.1155/2016/8426874 349 XiangS.LiuF.LinJ.ChenH.HuangC.ChenL.et al
Results: Seven studies were included: four randomized controlled trials, two quasi-experimental studies, and one developmental study
269,270 Its utility is limited in patients with advanced CKD owing to safety concerns